Morphea en coup de sabre and hemifacial atrophy in an interdisciplinary approach

Authors

  • Agnieszka Wróblewska Postgraduate studies in "Aesthetics of the Face", Poznan University of Medical Sciences, Poland
  • Adriana Polańska Department of Dermatology and Venereology, Poznan University of Medical Sciences, Poland
  • Aleksandra Dańczak‑Pazdrowska Department of Dermatology, Poznan University of Medical Sciences, Poland
  • Ryszard Żaba Department of Dermatology and Venereology, Poznan University of Medical Sciences, Poland
  • Zygmunt Adamski Department of Dermatology, Poznan University of Medical Sciences, Poland
  • Teresa Metthews‑Brzozowska Department of Maxillofacial Orthopedics and Orthodontics, Poznan University of Medical Sciences, Poland
  • Joanna Wegner Department of Dermatology, University Medical Center Mainz, Germany

DOI:

https://doi.org/10.20883/jofa.35

Keywords:

morphea en coup de sabre, progressive hemifacial atrophy, Parry‑Romberg syndrome, Romberg disease, facial asymmetry

Abstract

The increase in the degree of fluctuation asymmetry is accompanied, among others, by diseases such as morphea en coup de sabre (morphea ECDS) or Parry‑Romberg syndrome (PHA). Patients suffering from them struggle not only with dermatological defects, but also with neurological, rheumatological, orthopedic, ophthalmological and dental symptoms. Morphological and functional disorders and craniofacial deformities related to them often generate psychosocial problems. The complexity of the issues to be solved proves the necessity of undertaking interdisciplinary actions aimed at developing objective diagnostic and therapeutic protocols, restoring (especially in pediatric patients) as close as possible to the correct developmental patterns, inhibiting the active phase of the disease and undertaking effective and aesthetically satisfying measures.

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Published

2020-12-31

How to Cite

1.
Wróblewska A, Polańska A, Dańczak‑Pazdrowska A, Żaba R, Adamski Z, Metthews‑Brzozowska T, Wegner J. Morphea en coup de sabre and hemifacial atrophy in an interdisciplinary approach. JoFA [Internet]. 2020 Dec. 31 [cited 2024 Mar. 28];3(2):97-107. Available from: https://jofa.ump.edu.pl/index.php/jofa/article/view/35

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